The syndrome of hemophagocytic lymphohistiocytosis in primary immunodeficiencies
- Slides: 6
The syndrome of hemophagocytic lymphohistiocytosis in primary immunodeficiencies: implications for differential diagnosis and pathogenesis by Sebastian FN Bode, Sandra Ammann, Waleed Al-Herz, Mihaela Bataneant, Christopher C Dvorak, Stephan Gehring, Andrew Gennery, Kimberly C Gilmour, Luis I Gonzalez-Granado, Ute Groß-Wieltsch, Marianne Ifversen, Jenny Lingman. Framme, Susanne Matthes-Martin, Rolf Mesters, Isabelle Meyts, Joris M van Montfrans, Jana Pachlopnik Schmid, Sung-Yun Pai, Pere Soler-Palacin, Uta Schuermann, Volker Schuster, Markus G. Seidel, Carsten Speckmann, Polina Stepensky, Karl-Walter Sykora, Bianca Tesi, Thomas Vraetz, Catherine Waruiru, Yenan T. Bryceson, Despina Moshous, Kai Lehmberg, Michael B Jordan, and Stephan Ehl haematol Volume 100(7): 978 -988 June 30, 2015 © 2015 by Ferrata Storti Foundation
Cohort of patients with HLH syndrome in the context of primary immunodeficiencies. Sebastian FN Bode et al. Haematologica 2015; 100: 978 -988 © 2015 by Ferrata Storti Foundation
Lymphocyte subsets in patients with SCID and hemophagocytic inflammatory syndrome. Sebastian FN Bode et al. Haematologica 2015; 100: 978 -988 © 2015 by Ferrata Storti Foundation
(A) Serum s. CD 25 levels in patients with SCID/CID, FHL, I-HLH (infection triggered “secondary” HLH), and CGD. (B) Serum ferritin levels in SCID/CID, FHL, I-HLH, and CGD patients. Sebastian FN Bode et al. Haematologica 2015; 100: 978 -988 © 2015 by Ferrata Storti Foundation
HLH diagnostic criteria in patients with PID and hemophagocytic inflammatory syndrome. Sebastian FN Bode et al. Haematologica 2015; 100: 978 -988 © 2015 by Ferrata Storti Foundation
(A) Serum triglyceride levels in SCID/CID, FHL, I-HLH, and CGD patients. Sebastian FN Bode et al. Haematologica 2015; 100: 978 -988 © 2015 by Ferrata Storti Foundation
