Nephrotic Syndrome MPGN MGN FSGS MCD Dr Robin
Nephrotic Syndrome MPGN MGN FSGS MCD Dr. Robin Chaudhary M. D. (Ayu) Assistant Professor Department of Kaumarbhritya
Definition It is a Collection of Symptoms due to damage to the Kidney or Nephrotic syndrome is a collection of symptoms that indicate kidney damage
Terminology MCD: Minimal Change Disease FSGS: Focal Segmental Glomerulosclerosis MGN: Membranous Glomerulonephrosis MPGN: Membranoproliferative Glomerulonephrosis
Nephrotic Syndrome Classification Primary Nephrotic Syndrome • Glomerular Disease that is limited to Kidney • Also Known as Peimary Glomerulonephrosis • Diagnosis of Exclusion Secondary Nephrotic Syndrome Underlying Condition/Cause that affects Kidnay & also other body organs/parts
Primany Glomerulonephrosis Based on the Cause Minimal Change Disease Most common in Childrens( 2 – 6 yrs) Focal Segmental Glomerulosclerosis Most common in childrens & Adolocent Membranous Glomerulonephrosis Most common in Adults Membranoproliferative Glomerulonephrosis Common in both Childrens & Adults
Diabetic Nephropathy Drugs Genetic Nephrotic Syndrome SLE/Lupus Nephritis Secondary Nephrotic Syndrome Cancer HIV Hepatitis B
Pathophysiology Primary/Secondary Causes Inflammation Hyalinization Protien/Albuminuria Flow in Interstetial Spaces Edema • • • Puffiness Under Eyes Pitting edema in legs Fluid in Lungs (Pleural Effusion) Fluid in Perietal Cavity (Ascites) Generalised Fluid Accumulation (Anasarca) Low Oncotic Pressure in Vessels(Vascular System) • Proteinuria • Hypoalbuminemia Hyperlipidemia (due to Lipoproteins)
Sign & Symptoms Proteinuria Hypoalbuminemia Hyperlipidemia • Mainly Albumin • 40 g/m 2/body square meter/24 hr • <2. 5 g/dl • 3. 5 – 5 gm/dl (Normal) • Mainly LDL & VLDL
is gn os Dia Urine Analysis Blood Tests Kidney Biopsy Auto. Immune Markers
Treatment Hyperlipidemia * Medical Nutrition Hypoabuminemia *Medical Nutrition Edema * Medical Nutrition Therapy * Medication Therapy *Diet High in Animal Protein Therapy * Diet Low in Cholestrol
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