IDIOPATHIC BIG BLIND SPOT SYNDROME AND ACUTE ZONAL
IDIOPATHIC BIG BLIND SPOT SYNDROME AND ACUTE ZONAL OCCULT OUTER RETINOPATHY (AZOOR) Gölge Acaroğlu, Yasemin Özdamar, Özlem Aslan, Seyhan S. Özkan S. B Ankara Ulucanlar Eye Hospital golgeacaroglu@gmail. com
Case Report: • 29 y. o. F, • Slowly proggressive visual loss over 2 years. • VA: 0. 8 (OD), 0. 5 (OS) • Color vision full (OU) • Equal, reactive pupils, no RAPD • Anterior segment / vitreus normal • Brain / orbit MRI normal • CSF pressure normal • Systemic / neurological work-up normal.
Fundi: Bilateral discedema, mild temporal optic atrophy (OS), retina and vessels normal. FA: Leakage on the optic nerve heads.
Automated Static Visual Fields: Bilateral big blind spots.
Multifocal ERG: Bilateral macular depression.
Conclusion: • Presumed diagnosis of AZOOR was made and patient received immune supressive therapy. Symptoms and signs are improving. • Idiopathic big blind spot syndrome and retinal white dot syndromes are thought to be related to each other and their coexistance is termed as Acute Zonal Occult Outer Retinopathy (AZOOR). • AZOOR is a rare presumed autoimmune degeneration of outer retinal layers. It should be kept in mind in the differential diagnosis of young, otherwise healthy patients with papilledema and optic nerve dysfunction.
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