EhlersDanlos Syndrome EDS Is a connective tissue disorder

Ehlers-Danlos Syndrome (EDS) Ø Is a connective tissue disorder caused by a defect in collagen gene. Affects 1 in 5000 Ø The majority of EDS cases are clinically diagnosed by: • Joint Hypermobility/ TMJ Elasticity of skin Joint pain Easy bruising Dystrophic scarring Delayed healing • • •

Ehlers- Danlos Syndrome HYPERMOBILITY OF JOINTS ELASTICITY OF SKIN

Ehlers- Danlos Syndrome Ø Ø Extreme hypermobility often leads to chronic dislocation of the temporomandibular (jaw) joint (TMJ) TMJ problems can cause patients to grind or clench teeth ‘ Radiograph of TMJ Problems

Ehlers- Danlos Syndrome DYSTROPHIC SCARRING EASY BRUISING

Early onset of periodontal Disease • Individuals with classic EDS have an early onset of periodontitis • Periodontal disease is the irreversible destruction of periodontal ligaments and alveolar bone

Periodontal Disease in EDS • Gingival appearance seen in EDS patients : “thin translucent alveolar mucosa with swollen receded attached gingiva mainly on maxillary and mandibular premolars

Treatment of Periodontal Disease in EDS Without aggressive treatment of early onset of periodontal disease can lead to early tooth loss Edentulous Patient

Orthodontic apparatuses may also be used as a form of treatment depending on the integrity of the periodontal ligaments

Treatment of EDS • • THERE IS NO CURE!! Best practices for treating symptoms of EDS: ü Good Oral Hygiene and frequent recall Immediate medical attention for cuts or scars ü NSAIDs for joint pain ü

Referrals • Leslie Alan Goodman MD 3282 College Street. Beaumont, TX 77701 (409) 813 - 1677 • Reeti K Joshi MD 3030 North St. #450 Beaumont, TX 77702 (409) 832 -9600 • Vijay Kumar MD 3570 College Sr. Ste 200 Beaumont, TX 77701 (409) 833 9797 • Mary L Olsen MD 3030 North St. #450 Beaumont, TX 77702 (409) 832 -9600

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