CURRENT CONCEPTS IN THE DIAGNOSIS AND MANAGEMENT OF

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CURRENT CONCEPTS IN THE DIAGNOSIS AND MANAGEMENT OF VELOPHARYNGEAL DYSFUNCTION IN CHILDREN AND ADULTS

CURRENT CONCEPTS IN THE DIAGNOSIS AND MANAGEMENT OF VELOPHARYNGEAL DYSFUNCTION IN CHILDREN AND ADULTS MSHA 2013 PABLO ANTONIO YSUNZA antonio. ysunza@beaumont. edu

TERMINOLOGY • MALFORMATION: A LOCALIZED ERROR IN MORPHOGENESIS (CLEFT PALATE)

TERMINOLOGY • MALFORMATION: A LOCALIZED ERROR IN MORPHOGENESIS (CLEFT PALATE)

TERMINOLOGY • SEQUENCE: A MALFORMATION CAUSING ANOTHER MALFORMATION (S) • PIERRE-ROBIN SEQUENCE: MICROGNATHIA— GLOSSOPTOSIS—SUB-TOTAL

TERMINOLOGY • SEQUENCE: A MALFORMATION CAUSING ANOTHER MALFORMATION (S) • PIERRE-ROBIN SEQUENCE: MICROGNATHIA— GLOSSOPTOSIS—SUB-TOTAL PALATAL CLEFT) • Di. GEORGE SEQUENCE: NEURAL CREST DEFECT —THYMUS ABSENCE, HYPOCALCEMIA, IMMUNE DEFICIENCY

TERMINOLOGY • SYNDROME: GROUP OF MALFORMATIONS WITH COMMON ETIOLOGY (VELOCARDIOFACIAL SYNDROME-22 Q 11. 1

TERMINOLOGY • SYNDROME: GROUP OF MALFORMATIONS WITH COMMON ETIOLOGY (VELOCARDIOFACIAL SYNDROME-22 Q 11. 1 DELETION)

CLEFT PALATE • PRIMARY PALATE • SECONDARY PALATE

CLEFT PALATE • PRIMARY PALATE • SECONDARY PALATE

CLEFT PALATE

CLEFT PALATE

CLEFT PALATE

CLEFT PALATE

SUBMUCOUS CLEFT PALATE

SUBMUCOUS CLEFT PALATE

SUBMUCOUS CLEFT PALATE

SUBMUCOUS CLEFT PALATE

VPI • W / COMPENSATORY ARTICULATION ERRORS (HYPERNASALITY AND ABERRANT PLACEMENT AND MANNER) •

VPI • W / COMPENSATORY ARTICULATION ERRORS (HYPERNASALITY AND ABERRANT PLACEMENT AND MANNER) • WO / COMPENSATORY ARTICULATION ERRORS (HYPERNASALITY WITH APPROPRIATE PLACEMENT AND MANNER)

V P I + COMPENSATORY ERRORS • PROBLEM BEYOND V P S, INVOLVES ENTIRE

V P I + COMPENSATORY ERRORS • PROBLEM BEYOND V P S, INVOLVES ENTIRE VOCAL TRACT AND HIGHER LEVELS OF SPEECH PRODUCTION • SPEECH THERAPY IS INDICATED • 1/3 OF RESIDUAL V P I SHOW COMPENSATORY ERRORS • SURGERY DO NOT MODIFY COMPENSATORY ERRORS

VELOPHARYNGEAL SPHINCTER • ANTERIOR: VELUM (LEVATOR VELI PALATINI AND MUSCULUS UVULAE) • LATERAL: LATERAL

VELOPHARYNGEAL SPHINCTER • ANTERIOR: VELUM (LEVATOR VELI PALATINI AND MUSCULUS UVULAE) • LATERAL: LATERAL PHARYNGEAL WALLS (SUPERIOR PHARYNGEAL CONSTRICTOR) • POSTERIOR: POSTERIOR PHARYNGEAL WALL (SUPERIOR PHARYNGEAL CONSTRICTOR)

VIDEOFLUOROSCOPY • X-RAYS • DYNAMIC ASSESSMENT (VIDEO) • ANALYSIS ON VIDEO (DECREASE TOTAL RADIATION

VIDEOFLUOROSCOPY • X-RAYS • DYNAMIC ASSESSMENT (VIDEO) • ANALYSIS ON VIDEO (DECREASE TOTAL RADIATION TIME) • FRONTAL OR CORONAL, LATERAL OR SAGGITAL, BASE OR AXIAL

RESIDUAL V P I • SYNDROMIC • NON SYNDROMIC

RESIDUAL V P I • SYNDROMIC • NON SYNDROMIC

NON-SYNDROMIC V P I • INTRAVELAR VELOPLASTY (L V P SURGICAL REPAIR) • FURLOW

NON-SYNDROMIC V P I • INTRAVELAR VELOPLASTY (L V P SURGICAL REPAIR) • FURLOW Z PLASTY • PHARYNGEAL FLAP • SPHINCTER PHARYNGOPLASTY