BIRDSHOT CHORIORETINOPATHY CLINICAL SPECTRUM Cristina del Prado Snchez

BIRDSHOT CHORIORETINOPATHY: CLINICAL SPECTRUM. Cristina del Prado Sánchez Mº Carmen García Sáenz Pablo Gili Manzanaro Karla Gonzales Farro

CASES CASE 1 CASE 2 GENDER Man Woman AGE 66 years old 30 years old LATERALITY Bilateral INICIAL CLINIC Blurred vision, floaters, diminished color and contrast vision. INICIAL VISUAL ACUITY 0. 6/0. 8 1. 0/1. 0 FINAL VISUAL ACUITY hand movement/0. 6 0. 8/1. 0 HLA-A 29 Positive Negative FOLLOWING 10 years 12 years OUTBREAKS 3 8 COMPLICATIONS Right: macular hole, glaucoma, CME. Left: neovascular membrane. Both: macular pucker. Macular pucker, CME and macular atrophy. OUTBREAKS TREATMENT Systemic steroids - MAINTENANCE TREATMENT - DECLINED. Cyclosporine A. Azathioprine. Subconjunctival Triamcinolone. Systemic steroids.

CHOROIDES RETINA IMAGING STUDIES Retinography Fluorescein angiography • Yellowish lesions that radiate out from the optic nerve, more prominent on the nasal retina. • Early phase: hipoflurescent spots. • Late phase: hiperfluorescent spots. • Outbreaks: CME, vasculitis, optic nerve leakage Autofluorescence • Hipoautofluorescent areas. Indocianine green angiography • Early and midphase: hipofluorescent spots. OCT • Variations in the IS/OS line and maculopathy.

IMAGING STUDIES: CASE 1

OCT CASE 1

IMAGING STUDIES: CASE 2

OCT CASE 2

Retina Retinography and fluorescein angiography Choroides indocianine green angiography and autofluorescence Treatment Mostly clinical. Supported by the imaging studies for: Early diagnosis + outbreaks detection TREATMENT. Imaging studies Birdshot chorioretinopathy is a pathology with a wide clinical spectrum. Diagnosis Clinic CONCLUSIONS Is needed for: • Reducing ocular damage. • Inducing longterm remission. • Preserving visual acuity.

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